Morvan's Syndrome—A Case Report of a Rare Clinical Scenario

Dinesh Kumar; Saniya Kapila

doi:10.5005/jp-journals-10055-0056

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Morvan's Syndrome—A Case Report of a Rare Clinical Scenario

Dinesh Kumar, Saniya Kapila

Keywords : Agrypnia excitata, Antivoltage-gated potassium channel antibodies, Morvan's syndrome

Citation Information : Kumar D, Kapila S. Morvan's Syndrome—A Case Report of a Rare Clinical Scenario. Curr Trends Diagn Treat 2019; 3 (1):33-34.

DOI: 10.5005/jp-journals-10055-0056

License: CC BY-NC 4.0

Published Online: 01-06-2019

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Abstract

Background: Neuromyotonia is a disorder of peripheral nerve hyperexcitability, causing spontaneous muscular activity. It is an extremely rare disease. Infrequency with which it is encountered and nonspecific, vague symptoms in young people make it a formidable diagnostic challenge. Case description: We present a case of a 34-year-old male with complaints of twitching in muscles and pain in the thigh and calf region. These complaints occurred on and off since the last 6 months. He has a positive family history of similar symptoms. The patient was positive for serum voltage gated potassium channels (VGKC) antibodies. Electromyography (EMG) studies showed evidence of neuromyotonia. A diagnosis of Morvan's syndrome (neuromyotonia) was made on the basis of symptoms and EMG findings. The treatment of the patient was started on intravenous steroids, antiepileptics, and SSRI. Conclusion: Diagnosis of neuromyotonia is a challenge. Awareness among people is important to mitigate the symptoms and provide timely management.

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