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VOLUME 5 , ISSUE 1 ( January-June, 2021 ) > List of Articles


Atretic Cephalocele: Infrequent Cause of Cystic Scalp Swelling—A Case Report

Amandeep Singh, Aaina Devgan, Sumanjeet Kaur

Keywords : Atretic cephalocele, Magnetic resonance imaging, Scalp swelling

Citation Information : Singh A, Devgan A, Kaur S. Atretic Cephalocele: Infrequent Cause of Cystic Scalp Swelling—A Case Report. Curr Trends Diagn Treat 2021; 5 (1):42-44.

DOI: 10.5005/jp-journals-10055-0113

License: CC BY-NC 4.0

Published Online: 02-06-2021

Copyright Statement:  Copyright © 2021; The Author(s).


The degenerative form of encephalocele is termed as atretic cephalocele, which can be primarily seen in infants in the form of cystic mass lesion in the head. Patient generally presents with midline scalp swelling. It is usually characterized by the presence of many associated underlying intracranial malformations; therefore, prognosis varies. A 1-year-old girl child presented with a midline painless scalp swelling in the occipital region since 6 months which progressed gradually. The child otherwise was asymptomatic with normal developmental milestones. Magnetic resonance imaging findings revealed midline extra-axial altered signal intensity lesion in the occipital region with no underlying parenchymal extensions. Lesion is causing smooth scalloping of inner table of occiput. There is minimal enhancement on postcontrast images with no dural venous sinuses communication.

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